{"id":43458,"date":"2024-04-23T15:53:37","date_gmt":"2024-04-23T19:53:37","guid":{"rendered":"https:\/\/noti-america.com\/site\/principal\/?p=43458"},"modified":"2024-04-23T15:53:37","modified_gmt":"2024-04-23T19:53:37","slug":"dermatomiositis-juvenil-una-enfermedad-rara-inflamatoria-que-debuta-en-menores","status":"publish","type":"post","link":"https:\/\/noti-america.com\/site\/principal\/2024\/04\/23\/dermatomiositis-juvenil-una-enfermedad-rara-inflamatoria-que-debuta-en-menores\/","title":{"rendered":"Dermatomiositis juvenil: una enfermedad rara inflamatoria que debuta en menores"},"content":{"rendered":"<p>NOTI-AMERICA.COM | M\u00c9XICO \u2013 En el D\u00eda Nacional de la Dermatomiositis Juvenil, la Fundaci\u00f3n Espa\u00f1ola de Reumatolog\u00eda y la Asociaci\u00f3n Nacional de Dermatomiositis Juvenil (ANADEJU) insisten en la necesidad de dar mayor visibilidad a esta enfermedad, profundizar en la investigaci\u00f3n y garantizar una atenci\u00f3n multidisciplinar ((dermat\u00f3logos, oftalm\u00f3logos, cardi\u00f3logos, gastroenter\u00f3logos, rehabilitadores, psic\u00f3logos\u2026).<\/p>\n<p>Aproximadamente un 20 % de todas las dermatomiositis debutan en la edad pedi\u00e1trica, con un pico de incidencia entre los 5 y 14 a\u00f1os, como ocurre en el tipo juvenil y cuya incidencia es de 4 casos por cada mill\u00f3n de habitantes.<\/p>\n<h3 class=\"wp-block-heading\">\u00bfC\u00f3mo cursa la dermatomiositis juvenil?<\/h3>\n<p>Se trata de una\u00a0enfermedad autoinmune, por lo que es el propio sistema inmune del afectado el que provoca una inflamaci\u00f3n que ocasiona lesiones cut\u00e1neas y debilidad muscular.<\/p>\n<p>Es una patolog\u00eda cr\u00f3nica que aparece en brotes y tiene una intensidad variable.<\/p>\n<p>Seg\u00fan informa la\u00a0Fundaci\u00f3n Espa\u00f1ola de Reumatolog\u00eda, los ni\u00f1os y adolescentes que padecen dermatomiositis juvenil se pueden encontrar cansados y con dificultad para hacer ejercicio, incluso en fases m\u00e1s tard\u00edas pueden tener m\u00e1s dificultad para hacer actividades diarias habituales, como caminar distancias m\u00e1s largas, jugar o subir escaleras.<\/p>\n<p>Hay ni\u00f1os que sufren contracturas musculares o inflamaci\u00f3n de articulaciones, lo que puede producir dolor o dificultad en ciertos movimientos.<\/p>\n<p>Las lesiones cut\u00e1neas pueden aparecer antes que la inflamaci\u00f3n muscular. Habitualmente afecta a regiones como la cara, el escote y las manos, pero se pueden observar en cualquier parte del cuerpo.<\/p>\n<p>En pocas ocasiones pueden aparecer complicaciones como la calcinosis o\u00a0lipodistrofia. Otras manifestaciones como la afectaci\u00f3n pulmonar o card\u00edaca se observan en un n\u00famero escaso de ni\u00f1os.<\/p>\n<h3 class=\"wp-block-heading\">Atenci\u00f3n multidisciplinar<\/h3>\n<p>\u201cEs preciso un seguimiento estrecho y regular en las consultas de Reumatolog\u00eda para mantener un control adecuado de la enfermedad. Si bien, debido a que puede afectar a otros \u00f3rganos es imprescindible un abordaje multidisciplinar\u201d, afirma la\u00a0doctora Alina Boteanu, de la Unidad de Reumatolog\u00eda Pedi\u00e1trica del Hospital Universitario Ram\u00f3n y Cajal de Madrid.<\/p>\n<p>Tambi\u00e9n es fundamental el diagn\u00f3stico precoz y el tratamiento adecuado. \u201cEl desarrollo de varios f\u00e1rmacos y el aumento de opciones terap\u00e9uticas, junto con un tratamiento precoz, han llevado en los \u00faltimos a\u00f1os a una mejor\u00eda del pron\u00f3stico\u201d, afirma la reumat\u00f3loga.<\/p>\n<p>Para la presidenta de la Asociaci\u00f3n ANADEJU, Mar\u00eda del Carmen Miguel Rodr\u00edguez, tambi\u00e9n es importante el tratamiento psicol\u00f3gico: \u201cComo enfermedad cr\u00f3nica, el impacto negativo en ni\u00f1os, adolescentes, familiares y sociedad pone de manifiesto cada vez m\u00e1s la necesidad de la atenci\u00f3n psicol\u00f3gica\u201d.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>NOTI-AMERICA.COM | M\u00c9XICO \u2013 En el D\u00eda Nacional de la Dermatomiositis Juvenil, la Fundaci\u00f3n Espa\u00f1ola de Reumatolog\u00eda y la Asociaci\u00f3n Nacional de Dermatomiositis Juvenil (ANADEJU) insisten en la necesidad de dar mayor visibilidad a&#46;&#46;&#46;<\/p>\n","protected":false},"author":133,"featured_media":43459,"comment_status":"","ping_status":"open","sticky":false,"template":"","format":"image","meta":{"_acf_changed":false,"rop_custom_images_group":[],"rop_custom_messages_group":[],"rop_publish_now":"initial","rop_publish_now_accounts":{"facebook_10219548024599422_1632221337088128":"","twitter_242054905_242054905":""},"rop_publish_now_history":[],"rop_publish_now_status":"pending","footnotes":""},"categories":[663],"tags":[],"class_list":["post-43458","post","type-post","status-publish","format-image","has-post-thumbnail","hentry","category-actualidad","post_format-post-format-image"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v24.9 (Yoast SEO v27.2) - 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